246 III. DIGESTIBILITY OF FATS 



(6) Congenital Steatorrhea 



This condition is believed to be caused by the absence of pancreatic 

 lipase from the pancreatic juice; according to Garrod, 146 trypsin is present. 

 Congenital steatorrhea is an exceedingly rare condition, in which "butter 

 stools" are passed from birth. There are no other symptoms of pan- 

 creatic deficiency. Miller 147 suggested that this abnormality may occur 

 in early infancy. Barrit 148 has cited an interesting case of secondary 

 steatorrhea, following a gastroileal anastomosis, due to the exclusion of 

 the small intestine resulting from a faulty gastroenterostomy. 



146 A. E. Garrod, Inborn Errors of Metabolism, 2nd ed., Chap. IX, Oxford Univ. Press, 

 1923, pp. 166, 167. 



147 R. Miller, Proc. Roy. Soc. Med., Part I, Sect. Study Disease in Children, 16, 22-24 

 (1923). 



"• D. W. Barrit, Lancet, 263, 564-565 (1952). 



