Landau LI and Phelan PD. The variable effect of a bronchodilating agent on pulmonary function 
in cystic fibrosis. The variable effect of a bronchodilating agent on pulmonary function in cystic 
fibrosis. J Pediatr 1973; 82:863-868. 
McCray PB, Wohlford-Lenane CL, Snyder JM. Localization of cystic fibrosis transmembrane 
conductance regulator mRNA in human fetal lung tissue by in situ hybridization. J Clin Invest 
1992; 90:619-625. 
McElvaney NG, Nakamura H, Birrer P, Hebert CA, Wong WL, Alphonso M, Baker JB, 
Catalano MA, Crystal RG. Modulation of airway inflammation in cystic fibrosis: in vivo 
suppression of interleukin-8 levels on the respiratory epithelial surface by aerosolization of 
recombinant secretory leukoprotease inhibitor. J Clin Invest 1992; 90:1296-1301. 
McElvaney NG, Hubbard RC, Birrer P, Chemick MS, Caplan DB, Frank MM, Crystal RG. 
Aerosol alpha 1-antitrypsin treatment for cystic fibrosis. Lancet 1991; 337: 392-394 
Pasque MK, Cooper JD, Kaiser LR, et.al. Improved technique for bilateral lung transplantation: 
rationale and initial clinical experience. Ann Thorac Surg 1990; 49:785-791. 
Phipps PR, Gonda I, Bailey DL, Borham P, Bautovich G, Anderson SD. Comparisons of planar 
and tomographic gamma scintigraphy to measure the penetration index of inhaled aerosols. Am 
Rev Respir Dis 1989; 139:1516-1523. 
Regelmann WE, Elliott GR, Warwick WJ, Clawson CC. Reduction of sputum Pseudomonas 
aeruginosa density by antibiotics improves lung function in cystic fibrosis more than do 
bronchodilators and chest physiotherapy alone. Am Rev Respir Dis 1990; 141:914-921. 
Rich DP, Anderson MP, Gregory RJ, Cheng SH, Paul S, Jefferson DM, McCann JD, Klinger 
KW, Smith AE, Welsh MJ. Expression of cystic fibrosis transmembrane conductance regulator 
corrects defective chloride channel regulation in cystic fibrosis airway epithelial cells. Nature 
1990; 347: 358-363 
Riordan JR, Rommens JM, Kerem BS, Alon N, Rozmahel R, Grzelczak Z, Zielenski J, Lok S, 
Plavsic N, Chou JL, Drumm ML, Iannuzzi MC, Collins FS, Tsui L-C. Identification of the 
cystic fibrosis gene: cloning and characterizationn of complementary DNA. Science 1989; 245: 
1066-1073 
Roden AT, Pereira HG, Chaproniere DM. Infection of volunteers by a virus (A.P.C. type 1) 
isolated from human adenoid tissue. Lancet 1956; 2: 592-596 
Rommens JM, Iannuzzi MC, Kerem BS, Drumm ML, Melmer G, Dean M, Rozmahel R, Cole 
JL, Kennedy D, Hidaka N, Zsiga M, Buchwald M, Riordan JR, Tsui L-C, Collins FS. 
Identification of the cystic fibrosis gene: chromosome walking and jumping. Science 1989; 245: 
1059-1065 
Rosenfeld MA, Siegfried W, Yoshimura K, Yoneyama K, Fukayama M, Stier LE, Paakko PK, 
Gilardi P, Stratford-Perricaudet LD, Perricaudet M, Jallat S, Pavirani A, Lecocq J-P, Crystal 
Recombinant DNA Research, Volume 17 
[409] 
